ISSN: 2148-4902 | E-ISSN: 2536-4553
Giant Composite Pheochromocytoma and Gastrointestinal stromal tumor in a patient with Neurofibromatosis: A case report [North Clin Istanb]
North Clin Istanb. Ahead of Print: NCI-37431 | DOI: 10.14744/nci.2020.37431

Giant Composite Pheochromocytoma and Gastrointestinal stromal tumor in a patient with Neurofibromatosis: A case report

Soykan Arıkan1, Cihad Tatar1, Ali Emre Naycı1, Feyzullah Ersoz1, Mehmet Baki Dogan1, Feray Günver2
1Istanbul Training and Research Hospital, Department of General Surgery, Istanbul, Turkey
2Istanbul Training and Research Hospital, Department of Pathology, Istanbul, Turkey

A 54-year-old male was admitted to our department with neurofibromatosis and hypertension. During his examination, a mass was detected in the abdomen, and he was transferred to a surgical clinic. At the first examination of the patient, extensive café au lait spots and granulomas were detected on the body and the mass occupying right abdomen quadrant was palpable.
The patient’s medical history indicated that he had hypertension for almost a decade. The patient also stated that nodules on the body existed from his earliest recollection and he had relatives with neurofibromatosis. The patient was taken to a surgical operation. A mass with 30x23 cm in size was removed. The area of the nodular structure, with 0.5 cm in diameter, in the stomach seros was also removed. The tumor was composed of phaeochromocytoma in the larger spaces and ganglioneuromas in the relatively narrow spaces. The nodular area removed in gastric seros was reported as a very low-risk gastrointestinal stromal tumor.
Apart from this rare combination, adrenal mass removed from the patient was considerably larger than the masses in the literature until now. Therefore, we aimed to present this rare case with a literature background. (NCI-2019-0198.R2)

Keywords: Gastrointestinal stromal tumor, Pheochromocytoma, Neurofibromatosis



Corresponding Author: Cihad Tatar
Manuscript Language: English
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